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KMID : 1144020190150020173
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Journal of Korean Association for Disability and Oral Health
2019 Volume.15 No. 2 p.173 ~ p.178
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Dental management of Lowe syndrome under general anesthesia in a child: A case report
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Rhee Sophia
Song Ji-Soo
Shin Teo-Jeon
Kim Young-Jae
Kim Jung-Wook
Jang Ki-Taeg
Lee Sang-Hoon
Hyun Hong-Keun
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Abstract
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Lowe syndrome, also known as oculocerebrorenal syndrome, is a rare X-linked recessive disorder characterized by a combination of abnormalities associated with ocular (congenital cataracts), nervous system (mental impairment and hypotonia), and renal dysfunction. Dental crowding, over-retained primary teeth, ectopic and delayed eruption of permanent dentition, and taurodontism have been reported as oral findings. Dental care for young patients with Lowe syndrome is complicated by difficulties in behavior management and other systemic conditions of these patients. General anesthesia may be an appropriate and effective option to eliminate the need for repeated visits to the hospital and to provide improved treatment quality for the patient. However, this approach should be used with caution because general anesthesia may induce malignant hyperthermia and metabolic acidosis in patients with Lowe syndrome. This case study reports the dental management of Lowe syndrome in a 4-yearold male patient who presented with multiple caries in his primary dentition under general anesthesia.
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KEYWORD
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Lowe syndrome, Dental treatment, General anesthesia
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